Gastaut type idiopathic occipital epilepsy
https://doi.org/10.14412/2074-2711-2015-1S-19-21
Abstract
Idiopathic occipital epilepsy is a rare epileptic syndrome. Its incidence in a Novosibirsk cohort of patients with idiopathic focal epilepsy is 0.9%.
Objective: to present a clinical description of new cases of Gastaut syndrome, the types of its course, and treatment options in these patients.
Patients and methods. The study covers 17 cases of Gastaut type idiopathic occipital epilepsy in 13 women and 4 men aged 11–53 years.
Results. Among 17 cases we present 4 family cases with the disease. Three generations in 2 families were observed to have epilepsy, including Gastaut syndrome concurrent with childhood absence epilepsy. The adolescent onset of the disease was seen in most cases. Its main symptoms were focal visual seizures (100%), focal sensory seizures (58.9%), cephalalgia (47.1%), speech disorders (41.2%), and secondarily generalized convulsive seizures (35.3%). According to the frequency of seizures, the investigators identified 5 types of the course: single focal seizures, rare focal seizures with or without convulsions, frequent focal seizures with or without convulsions. The identity of the course of epilepsy was found in familial cases. 76.5% of the patients had a good quality of life: 41.2% of them were untreated while 35.3% were treated; no seizures were noted.
About the Authors
I. V. Volkov
Novosibirsk City Neurology Center «Sibneiromed», Novosibirsk, Russia; 37, Michurin St., Novosibirsk 630091;
Russian Federation
Russian Federation
O. K. Volkova
Novosibirsk City Neurology Center «Sibneiromed», Novosibirsk, Russia; 37, Michurin St., Novosibirsk 630091;
Children's Clinical Hospital Three, Novosibirsk, Russia; 81, Okhotskaya St., Novosibirsk 630040
Russian Federation
Russian Federation
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Review
For citations:
Volkov I.V., Volkova O.K. Gastaut type idiopathic occipital epilepsy. Neurology, Neuropsychiatry, Psychosomatics. 2015;7(1S):19-21. (In Russ.) https://doi.org/10.14412/2074-2711-2015-1S-19-21
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