References

nnp

Neurology, Neuropsychiatry, Psychosomatics

Неврология, нейропсихиатрия, психосоматика

2074-27112310-1342

"IMA-Press", LLC

10.14412/2074-2711-2018-3-91-96

nnp-955

Research Article

CLINICAL OBSERVATIONS

КЛИНИЧЕСКИЕ НАБЛЮДЕНИЯ

Benign syringomyelia with the abortive type of the course

Доброкачественный вариант сирингомиелии с абортивным типом течения

Менделевич

Е. Г.

Mendelevich

E. G.

Кафедра неврологии и реабилитации

Department of Neurology and Rehabilitation

Нуруллина

Ч. С.

Nurullina

Ch. S.

Кафедра неврологии и реабилитации

Department of Neurology and Rehabilitation

chulpan_nurullina@mail.ru

ФГБОУ ВО «Казанский государственный медицинский университет», Казань, Республика ТатарстанРоссияKazan State Medical University, Kazan, Republic of TatarstanRussian Federation

2018

08112018

1039196

2018

Менделевич Е.Г., Нуруллина Ч.С.

Mendelevich E.G., Nurullina C.S.

Данная работа распространяется под лицензией Creative Commons Attribution 4.0.

This work is licensed under a Creative Commons Attribution 4.0 License.

https://nnp.ima-press.net/nnp/article/view/955

Syringomyelia is a chronic disease with progressive cavitation and clinical presentations of spinal cord injury. The paper describes clinical cases of a rare benign variant of syringomyelia with spontaneous cavity collapse. The peculiarity of the described clinical cases is childhood-onset of the disease, lack of progression and/or development of myelopathic symptoms, and signs of syringomyelia cavity collapse according to magnetic resonance imaging findings. The authors designate this childhood-onset variant of the disease as abortive. The tendency towards collapse in the cavity in these patients may be due to a single pathogenetic mechanism, which is of interest for a further investigation.

Сирингомиелия – хроническое заболевание с прогрессирующим развитием полости и клинической картиной поражения спинного мозга. Представлены клинические наблюдения редкого доброкачественного варианта течения сирингомиелии со спонтанным спадением полости. Особенностью описанных клинических наблюдений является начало заболевания в детском возрасте, отсутствие прогрессирования и/или развития миелопатических симптомов, признаки спадения сирингомиелической полости по данным магнитно-резонансной томографии. Подобный вариант течения болезни с началом в детском возрасте обозначен нами как абортивный. Склонность к спадению полости у данных пациентов может быть обусловлена единым патогенетическим механизмом, что представляет интерес для дальнейшего изучения.

сирингомиелиямальформация Киариспонтанный коллапсмагнитно-резонансная терапиязадняя черепная ямка

syringomyeliaChiari malformationspontaneous collapsemagnetic resonance imagingposterior cranial fossa

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The authors declare that there are no conflicts of interest present.