nnpNeurology, Neuropsychiatry, PsychosomaticsНеврология, нейропсихиатрия, психосоматика2074-27112310-1342"IMA-Press", LLC10.14412/2074-2711-2018-1S-31-37nnp-906Research ArticleORIGINAL INVESTIGATIONSОРИГИНАЛЬНЫЕ ИССЛЕДОВАНИЯ И МЕТОДИКИJuvenile myoclonic epilepsy: neurophysiological aspectsНейрофизиологические аспекты юношеской миоклонической эпилепсииШилкинаО. С.ShilkinaO. S.

660022, Красноярск, ул. Партизана Железняка, 1

1, Partisan Zheleznyak St., Krasnoyarsk, 660022

ШнайдерН. А.ShnaiderN. A.

660022, Красноярск, ул. Партизана Железняка, 1

192019, Санкт-Петербург, ул. Бехтерева, 3

1, Partisan Zheleznyak St., Krasnoyarsk, 660022

3, Bekhterev St., Saint Petersburg 192019

NASchnaider@yandex.ruДмитренкоД. В.DmitrenkoD. V.

660022, Красноярск, ул. Партизана Железняка, 1

1, Partisan Zheleznyak St., Krasnoyarsk, 660022

КимК. Т.KimK. T.

660022, Красноярск, ул. Партизана Железняка, 1

1, Partisan Zheleznyak St., Krasnoyarsk, 660022

ФГБОУ ВО «Красноярский государственный медицинский университет им. проф. В.Ф. Войно-Ясенецкого» Минздрава РоссииРоссияProf. V.F. Voino-Yasenetsky Krasnoyarsk State Medical University, Ministry of Health of RussiaRussian FederationФГБОУ ВО «Красноярский государственный медицинский университет им. проф. В.Ф. Войно-Ясенецкого» Минздрава России ФГБУ «Национальный медицинский исследовательский центр неврологии и психиатрии им. В.М. Бехтерева» Минздрава РоссииРоссияProf. V.F. Voino-Yasenetsky Krasnoyarsk State Medical University, Ministry of Health of Russia V.M. Bekhterev National Medical Research Center, of Psychiatry and Neurology, Ministry of Health of RussiaRussian Federation201817072018101SСПЕЦВЫПУСК: ЭПИЛЕПСИЯ3137Copyright © Shilkina O.S., Shnaider N.A., Dmitrenko D.V., Kim K.T., 20182018Шилкина О.С., Шнайдер Н.А., Дмитренко Д.В., Ким К.Т.Shilkina O.S., Shnaider N.A., Dmitrenko D.V., Kim K.T.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://nnp.ima-press.net/nnp/article/view/906

The review presents an update on the electroencephalographic characteristics and neurophysiology of juvenile myoclonic epilepsy (JME) in Russia and foreign countries.

Materials and methods

Materials and methods. The authors have performed a literary search for the full-text publications on JME electroencephalography and neurophysiology worldwide and in the Russian Federation, which are available in Russian and foreign databases.

Results and discussion

Results and discussion. Analysis of the literature suggests that JME patients have some electroencephalographic pattern features that include the atypical morphology of spike-and-slow-wave  complexes, as well as amplitude asymmetry, focal discharges, focal  onset of paroxysms, focal paroxysmal shift, and generalized paroxysmal fast rhythm.The analysis of the literature also indicates that primary care neurologists, clinical neurophysiologists, and epileptologists should be informed about the electroencephalographic characteristics of JME to timely diagnose the disease and to rule out the use of inadequate therapy.

Изложены современные сведения об электроэнцефалографических особенностях юношеской миоклонической эпилепсии (ЮМЭ), современные данные о нейрофизиологии ЮМЭ в России и за рубежом.

Материалы и методы

Материалы и методы. Проведен литературный поиск доступных полнотекстовых публикаций, посвященных электроэнцефалографии и нейрофизиологии ЮМЭ в мире и в Российской Федерации, в российских и зарубежных базах данных.

Результаты и обсуждение

Результаты и обсуждение. Анализ литературы показал наличие особенностей паттерна электроэнцефалографии у больных ЮМЭ, к которым следует отнести атипичную  морфологию комплексов спайк-медленная волна, амплитудную асимметрию, фокальные  разряды, фокальное начало пароксизмов, фокальное смещение пароксизмов и наличие  генерализованного пароксизмального быстрого ритма.Анализ литературы свидетельствует о необходимости информирования врачей неврологов первичного звена здравоохранения, клинических нейрофизиологов, эпилептологов об  электроэнцефалографических особенностях ЮМЭ с целью своевременной диагностики заболевания, исключения назначения неадекватной терапии.

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The authors declare that there are no conflicts of interest present.