nnpNeurology, Neuropsychiatry, PsychosomaticsНеврология, нейропсихиатрия, психосоматика2074-27112310-1342"IMA-Press", LLC10.14412/2074-2711-2018-1-90-95nnp-838Research ArticleREVIEWSОБЗОРЫCranial dystoniaКраниальная дистонияТолмачеваВ. А.TolmachevaV. A.

Кафедра нервных болезней и нейрохирургии,

119021, Москва, ул. Россолимо, 11

Department of Nervous System Diseases and Neurosurgery, 

111, Rossolimo St., Moscow 119021

vtolmacheva@yandex.ruФГАОУ ВО «Первый Московский государственный медицинский университет им. И.М. Сеченова (Сеченовский университет)» Минздрава РоссииРоссияI.M. Sechenov First Moscow State Medical University (Sechenov University), Ministry of Health of RussiaRussian Federation2018020420181019095Copyright © Tolmacheva V.A., 20182018Толмачева В.А.Tolmacheva V.A.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://nnp.ima-press.net/nnp/article/view/838

Cranial dystonia is a common disease of the extrapyramidal nervous system. The clinical manifestations of dystonia are extremely variable; many of its forms are often undiagnosed. Dystonia is a sensorimotor disorder of the nervous system. Damage affects not only one structure, but also a network of the nodes interacting with each other in the somatosensory cortex and associative sensory and motor fields, which play a role in the integration of various sensory modalities coming from both outside the body and from the receptors within it. Botulinum toxin preparations show the highest efficacy in treating cranial dystonia. If their administration cannot achieve a positive result, oral drugs and surgical treatments should be used.

Краниальная дистония – распространенное заболевание экстрапирамидной нервной системы. Клинические проявления дистонии крайне вариабельны, многие ее формы часто не диагностируются. Дистония представляет собой сенсомоторное нарушение нервной системы. Повреждение затрагивает не одну структуру, а сеть взаимодействующих друг с другом узлов, расположенных в соматосенсорной коре и ассоциативных сенсорных и моторных полях, которые играют роль в интеграции различных сенсорных модальностей, поступающих как извне, так и от рецепторов внутри организма. При краниальной дистонии максимальной эффективностью отличаются препараты ботулотоксина. Если при их применении не удается достигнуть положительного результата, используют пероральные лекарственные средства и хирургические методы лечения.

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The authors declare that there are no conflicts of interest present.