nnpNeurology, Neuropsychiatry, PsychosomaticsНеврология, нейропсихиатрия, психосоматика2074-27112310-1342"IMA-Press", LLC10.14412/2074-2711-2020-2-79-85nnp-1309Research ArticleCLINICAL OBSERVATIONSКЛИНИЧЕСКИЕ НАБЛЮДЕНИЯNeurocutaneous melanosis concurrent with a posterior cranial fossa cyst (Dandy–Walker complex) and an intradural arachnoid cyst of the spinal canalНейрокожный меланоз в сочетании с кистой задней черепной ямки (комплекс Денди–Уокера) и интрадуральной арахноидальной кистой позвоночного каналаЕвзиковГ. Ю.EvzikovG. Yu.
11, Rossolimo St, Build. 1, Moscow 119021, Russia
БашлачевМ. Г.BashlachevM. G.bashlachev.m@gmail.comШашковаЕ. В.ShashkovaE. V.БелозерскихК. А.BelozerskikhK. A.ГребеневФ. В.GrebenevF. V.Кафедра нервных болезней и нейрохирургии;
Клиника нервных болезней Института клинической медицины ФГАОУ ВО «Первый Московский государственный медицинский университет им. И.М. Сеченова» Минздрава России (Сеченовский университет)РоссияDepartment of Nervous System Diseases and Neurosurgery;
Clinic for Nervous System Diseases, Institute of Clinical Medicine, I.M. Sechenov First Moscow State Medical University (Sechenov University), Ministry of Health of RussiaRussian FederationКлиника нервных болезней Института клинической медицины ФГАОУ ВО «Первый Московский государственный медицинский университет им. И.М. Сеченова» Минздрава России (Сеченовский университет)РоссияClinic for Nervous System Diseases, Institute of Clinical Medicine, I.M. Sechenov First Moscow State Medical University (Sechenov University), Ministry of Health of RussiaRussian Federation2020180420201227985Copyright © Evzikov G.Y., Bashlachev M.G., Shashkova E.V., Belozerskikh K.A., Grebenev F.V., 20202020Евзиков Г.Ю., Башлачев М.Г., Шашкова Е.В., Белозерских К.А., Гребенев Ф.В.Evzikov G.Y., Bashlachev M.G., Shashkova E.V., Belozerskikh K.A., Grebenev F.V.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://nnp.ima-press.net/nnp/article/view/1309аномалия Денди–Уокеранейрокожный меланозспинальная арахноидальная кистаDandy–Walker anomalyneurocutaneous melanosisspinal arachnoid cystReferencesБелопасов ВВ, Сопрунова ИВ, Цоцонава ЖМ, Ажкамалов СИ. Болезнь Рокитанского (Нейрокожный Меланоз). Нейрохирургия и неврология детского возраста. 2012;(2-3):36-43.Belopasov VV, Soprunova IV, Tsotsonava ZhM, Azhkamalov SI. Rokitansky's Disease (Neurocutaneous Melanosis). Neirokhirurgiya i nevrologiya detskogo vozrasta. 2012;(2-3): 36-43. (In Russ.).Kadonaga JN, Barkovich AJ, Edwards MS, Frieden IJ. Neurocutaneous melanosis in association with the Dandy–Walker complex. Pediatr Dermatol. 1992 Mar;9(1):37-43.Kadonaga JN, Barkovich AJ, Edwards MS, Frieden IJ. Neurocutaneous melanosis in association with the Dandy–Walker complex. Pediatr Dermatol. 1992 Mar;9(1):37-43.Ramaswamy V, Delaney H, Haque S, et al. Spectrum of central nervous system abnormalities in neurocutaneous melanocytosis. Dev Med Child Neurol. 2012 Jun;54(6):563-8. doi: 10.1111/j.1469-8749.2012.04275.x. Epub 2012 Apr 2.Ramaswamy V, Delaney H, Haque S, et al. Spectrum of central nervous system abnormalities in neurocutaneous melanocytosis. Dev Med Child Neurol. 2012 Jun;54(6):563-8. doi: 10.1111/j.1469-8749.2012.04275.x. Epub 2012 Apr 2.DeDavid M, Orlow SJ, Provost N, et al. Neurocutaneous melanosis: clinical features of large congenital melanocytic nevi in patients with manifest central nervous system melanosis. J Am Acad Dermatol. 1996 Oct;35(4):529-38.DeDavid M, Orlow SJ, Provost N, et al. Neurocutaneous melanosis: clinical features of large congenital melanocytic nevi in patients with manifest central nervous system melanosis. J Am Acad Dermatol. 1996 Oct;35(4):529-38.Kinsler VA, Thomas AC, Ishida M, et al. Multiple congenital melanocytic nevi and neurocutaneous melanosis are caused by postzygotic mutations in codon 61 of NRAS. J Invest Dermatol. 2013 Sep;133(9):2229-36. doi: 10.1038/jid.2013.70. Epub 2013 Feb 7.Kinsler VA, Thomas AC, Ishida M, et al. Multiple congenital melanocytic nevi and neurocutaneous melanosis are caused by postzygotic mutations in codon 61 of NRAS. J Invest Dermatol. 2013 Sep;133(9):2229-36. doi: 10.1038/jid.2013.70. Epub 2013 Feb 7.Salgado CM, Basu D, Nikiforova M, et al. 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Neurocutaneous melanosis and the Dandy–Walker complex: an uncommon but not so insignificant association. Childs Nerv Syst. 2009 Dec;25(12):1533-9. doi: 10.1007/s00381-009-0976-6. Epub 2009 Aug 27.Doroshenko MB, Utyashev IA, Demidov LV, Aliev MD. linical and biological features of giant congenital nevi in children. Pediatriya. Zhurnal im. G.N. Speranskogo. 2016;(4): 50-6. (In Russ.).Foster RD, Williams ML, Barkovich AJ, et al. Giant congenital melanocytic nevi: the significance of neurocutaneous melanosis in neurologically asymptomatic children. Plast Reconstr Surg. 2001 Apr 1;107(4):933-41.Marnet D, Vinchon M, Mostofi K, et al. Neurocutaneous melanosis and the Dandy–Walker complex: an uncommon but not so insignificant association. Childs Nerv Syst. 2009 Dec;25(12):1533-9. doi: 10.1007/s00381-009-0976-6. Epub 2009 Aug 27.Lovett A, Maari C, Decarie JC, Marcoux D, et al. Large congenital melanocytic nevi and neurocutaneous melanocytosis: one pediatric center's experience. J Am Acad Dermatol. 2009 Nov;61(5):766-74. doi: 10.1016/j.jaad.2008.11.022. Epub 2009 Sep 18.Foster RD, Williams ML, Barkovich AJ, et al. Giant congenital melanocytic nevi: the significance of neurocutaneous melanosis in neurologically asymptomatic children. Plast Reconstr Surg. 2001 Apr 1;107(4):933-41.Agero AL, Benvenuto-Andrade C, Dusza SW, et al. Asymptomatic neurocutaneous melanocytosis in patients with large congenital melanocytic nevi: a study of cases from an Internet-based registry. J Am Acad Dermatol. 2005 Dec;53(6):959-65. Epub 2005 Oct 7.Lovett A, Maari C, Decarie JC, Marcoux D, et al. Large congenital melanocytic nevi and neurocutaneous melanocytosis: one pediatric center's experience. J Am Acad Dermatol. 2009 Nov;61(5):766-74. doi: 10.1016/j.jaad.2008.11.022. Epub 2009 Sep 18.Takayama H, Nagashima Y, Hara M, et al. Immunohistochemical detection of the c-met proto-oncogene product in the congenital melanocytic nevus of an infant with neurocutaneous melanosis. J Am Acad Dermatol. 2001 Mar;44(3):538-40.Agero AL, Benvenuto-Andrade C, Dusza SW, et al. Asymptomatic neurocutaneous melanocytosis in patients with large congenital melanocytic nevi: a study of cases from an Internet-based registry. J Am Acad Dermatol. 2005 Dec;53(6):959-65. Epub 2005 Oct 7.Di Rocco F, Sabatino G, Koutzoglou M, et al. Neurocutaneous melanosis. Childs Nerv Syst. 2004 Jan;20(1):23-8. Epub 2003 Oct 24.Takayama H, Nagashima Y, Hara M, et al. Immunohistochemical detection of the c-met proto-oncogene product in the congenital melanocytic nevus of an infant with neurocutaneous melanosis. J Am Acad Dermatol. 2001 Mar;44(3):538-40.Barkovich A, Frieden I, Williams M. MR of neurocutaneous melanosis. AJNR Am J Neuroradiol. 1994 May;15(5):859-67.Di Rocco F, Sabatino G, Koutzoglou M, et al. Neurocutaneous melanosis. Childs Nerv Syst. 2004 Jan;20(1):23-8. Epub 2003 Oct 24.Chaloupka J, Wolf R, Varma P. 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The authors declare that there are no conflicts of interest present.